3-Methylglutaric acid, a leucine metabolite, is a conspicuous C6 dicarboxylic organic acid classically associated with two distinct leucine pathway enzyme deficiencies, 3-hydroxy-3-methylglutaryl CoA lyase (HMGCL) and 3-methylglutaconyl CoA hydratase (AUH).
IC50&Target
Human Endogenous Metabolite
分子式
C6H10O4
分子量
146.14
CAS号
626-51-7
中文名称
3-甲基戊二酸
运输条件
Room temperature in continental US; may vary elsewhere.