3-Methylglutaconic Acid
(Synonyms:3-甲基戊烯二酸;五氟苯基二苯基膦酸酯)
目录号 : KG10513
CAS No. : 5746-90-7
纯度 : >95%
3-Methylglutaconic acid (3-MGA) is a branched-chain organic acid and product of leucine catabolism.3-MGA accumulates in 3-methylglutaconic aciduria, which is caused by an inborn error of leucine metabolism characterized by 3-MGA-CoA hydratase deficiency, leading to delayed development, hypoglycemia, metabolic acidosis, and neurological impairments.
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分子式 |
C6H8O4
|
分子量 |
144.1
|
CAS号 |
5746-90-7
|
中文名称 |
五氟苯基二苯基膦酸酯
|
储存方式 |
Powder |
-20°C |
3 years |
|
4°C |
2 years |
In solvent |
-80°C |
6 months |
|
-20°C |
1 month |
|